Restrictive chest bellows disease and frontometaphyseal dysplasia.
نویسندگان
چکیده
We describe a patient with frontometaphyseal dysplasia (FMD), restrictive chest bellows disease, hypercapnic respiratory failure, and cor pulmonale. Treatment with intermittent supplemental oxygen, nocturnal nasal volume ventilation, and posture modification was successful in partial resolution of chronic hypoventilation and excessive daytime somnolence.
منابع مشابه
Frontometaphyseal dysplasia: autosomal dominant or X-linked?
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ورودعنوان ژورنال:
- Chest
دوره 103 4 شماره
صفحات -
تاریخ انتشار 1993